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NCT04669535 · ClinicalTrials.gov registry record · Phase 1

A Dose-escalation and Safety & Efficacy Study of AXO-AAV-GM2 in Tay-Sachs or Sandhoff Disease

A Phase 1 study, sponsored by Terence Flotte.

Terminated
Registry status
Phase 1
Development phase
9
Enrollment target

NCT04669535 is a Phase 1 study that was terminated before completion, run by Terence Flotte. The registered enrollment target is 9 participants.

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The verdict

NCT04669535, a Phase 1 study, was terminated before completion, sponsored by Terence Flotte.

TERMINATED
Registry status
Phase 1
Development phase
9 participants
Enrollment target

Study Summary

The AXO-GM2-001 study is an open-label, two-stage clinical trial designed to evaluate safety and dose-escalation (Stage 1) and safety and efficacy (Stage 2) of a bilateral thalamic and intracisternal/intrathecal infusion of AXO-AAV-GM2 in pediatric participants with GM2 Gangliosidosis (also known as Tay-Sachs or Sandhoff Diseases), a set of rare and fatal pediatric neurodegenerative genetic disorders caused by defects in the HEXA (leading to Tay-Sachs disease) or HEXB (leading to Sandhoff disease) genes that encode the two subunits of the β-hexosaminidase A (HexA) enzyme. AXO-AAV-GM2 is an investigational gene therapy that aims to restore HexA function by introducing a functional copy of the HEXA and HEXB genes via co-administration of two vectors utilizing the neurotropic adeno-associated virus recombinant human 8 serotype (AAVrh.8) capsid carrying the human HEXA or HEXB cDNA. The trial is expected to enroll pediatric participants with Tay-Sachs or Sandhoff Diseases, where infantile-onset participants will range from 6 months to 20 months old, and juvenile-onset participants will range from 2 years to 12 years old.

Interventions

  • BIOLOGICAL AXO-AAV-GM2 Starting Dose
  • BIOLOGICAL AXO-AAV-GM2 Low Dose
  • BIOLOGICAL AXO-AAV-GM2 Middle Dose
  • BIOLOGICAL AXO-AAV-GM2 High Dose

Trial Details

FieldValue
Enrollment Target 9 participants
Start Date 2021-01-15
Est. Completion 2024-12-16
Phase Phase 1

Sponsor

Terence Flotte

2 total trials

What the Registry Record Tells You About NCT04669535

The ClinicalTrials.gov registry entry for NCT04669535 describes a study currently listed as terminated, categorized as Phase 1. The registered enrollment target is 9 participants, a figure that helps gauge the scale of data the investigators plan to collect. The listed sponsor is Terence Flotte, which has 2 total studies on file at ClinicalTrials.gov.

The record links to 0 conditions, and to 4 interventions - of which AXO-AAV-GM2 Starting Dose is the first listed.

NCT04669535 reports 0 study locations.

Frequently Asked Questions

What is clinical trial NCT04669535 about?

NCT04669535 is a clinical study titled "A Dose-escalation and Safety & Efficacy Study of AXO-AAV-GM2 in Tay-Sachs or Sandhoff Disease". The AXO-GM2-001 study is an open-label, two-stage clinical trial designed to evaluate safety and dose-escalation (Stage 1) and safety and efficacy (Stage 2) of a bilateral thalamic and intracisternal/intrathecal infusion of AXO-AAV-GM2 in pediatric participants with GM2 Gangliosidosis (also known as...

What is the current status of trial NCT04669535?

This trial is currently terminated. It is a Phase 1 study. The enrollment target is 9 participants. The study started on 2021-01-15. Estimated completion is 2024-12-16.

What interventions are being tested in trial NCT04669535?

The interventions under investigation include: AXO-AAV-GM2 Starting Dose (BIOLOGICAL), AXO-AAV-GM2 Low Dose (BIOLOGICAL), AXO-AAV-GM2 Middle Dose (BIOLOGICAL), AXO-AAV-GM2 High Dose (BIOLOGICAL).

Who is sponsoring clinical trial NCT04669535?

This trial is sponsored by Terence Flotte, which has 2 total clinical trials registered on ClinicalTrials.gov.

Data sourced from official public datasets. See our methodology for details. Retrieved and formatted by PlainTrial Editorial

Every figure on PlainTrial is rendered directly from the ClinicalTrials.gov registry, no number is typed in by an editor. This page mirrors this trial's own ClinicalTrials.gov registry record, live from the dataset. See our editorial standards & corrections policy, the methodology behind these numbers, or report a data error.