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NCT01425528 · ClinicalTrials.gov registry record · Phase 1

Study of Kuvan Treatment in Adults With GTPCH Deficiency

A Phase 1 study, sponsored by University of Utah.

Completed
Registry status
Phase 1
Development phase
12
Enrollment target

NCT01425528: Completed Phase 1 study, sponsored by University of Utah.

NCT01425528 is a Phase 1 study that has completed, run by University of Utah. The registered enrollment target is 12 participants, below the 60-participant average among 29,502 other Phase 1 trials with a reported enrollment target (80% lower). According to ClinicalTrials.gov, the official US trial registry.

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The verdict

NCT01425528, a Phase 1 study, has completed, sponsored by University of Utah.

COMPLETED
Registry status
Phase 1
Development phase
12 participants
Enrollment target

Study Summary

The purpose of this study is to identify the dose of Kuvan needed to normalize the levels of tetrahydrobiopterin (BH4) in patients with a Guanosine Triphosphate Cyclohydrolase (GTPCH) deficiency and to asses the potential impact of oral Kuvan on mood and function in individuals with GTPCH deficiency who may be experiencing symptoms of anxiety, depression, fatigue, trouble concentrating, or memory loss. This will be a phase one study. The investigators will monitor patients over a period of three to six months while on the medication. Medication levels will be monitored by measuring the BH4 levels in cerebral spinal fluid (CSF). Patients will undergo a baseline lumbar puncture and two follow-up lumbar punctures for this purpose. The investigators will also monitor emotional function and motor function.

Primary Outcome

Identify dosing range of oral Kuvan® necessary and sufficient to normalize CSF BH4 levels in adults with GTPCH Deficiency.

Interventions

  • DRUG Sapropterin

Trial Details

FieldValue
Enrollment Target 12 participants
Start Date 2011-08
Est. Completion 2013-08
Phase Phase 1
University of Utah

818 total trials

What the finished NCT01425528 record still lists

NCT01425528 is an interventional study that assigns participants to a tested intervention. The registry caps enrollment at 12 participants, a relatively small participant target, below the 60-participant average among 29,502 other Phase 1 trials with a reported enrollment target (80% lower).

The record links to 0 conditions, and to 1 intervention - of which Sapropterin is the first listed.

NCT01425528 does not publish any study locations in the registry export this page uses.

Frequently Asked Questions

What is clinical trial NCT01425528 about?

NCT01425528 is a clinical study titled "Study of Kuvan Treatment in Adults With GTPCH Deficiency". The purpose of this study is to identify the dose of Kuvan needed to normalize the levels of tetrahydrobiopterin (BH4) in patients with a Guanosine Triphosphate Cyclohydrolase (GTPCH) deficiency and to asses the potential impact of oral Kuvan on mood and function in individuals with GTPCH deficiency...

What is the current status of trial NCT01425528?

This trial is currently completed. It is a Phase 1 study. The enrollment target is 12 participants. The study started on 2011-08. Estimated completion is 2013-08.

What interventions are being tested in trial NCT01425528?

The interventions under investigation include: Sapropterin (DRUG).

Who is sponsoring clinical trial NCT01425528?

This trial is sponsored by University of Utah, which has 818 total clinical trials registered on ClinicalTrials.gov.

How this trial's enrollment target compares

Where NCT01425528's enrollment target sits among peer trials

12 1852nd of 2000 higher than 90 of 2,000 other Phase 1 trials

participants (enrollment target), bucketed by value

Each bar is a band; taller bars hold more other Phase 1 trials. The dashed line + filled bar mark this entry. Hover or tap any bar for its full count and share, and where it sits relative to this entry.

Source ClinicalTrials.gov registry export · 2026-08-08

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Source: ClinicalTrials.gov NCT01425528, the US trial registry maintained by the National Library of Medicine. NCT01425528 (small enrollment · none site footprint · completed) retrieved and formatted by PlainTrial, see methodology.